Primitive neuroectodermal tumor of the cervix uteri
Synonyms: Cervical malignant peripheral neuroectodermal tumor | Cervical peripheral neuroectodermal cancer | Malignant peripheral neuroectodermal tumor of the cervix uteri | Peripheral neuroectodermal cancer of cervix uteri
Primitive neuroectodermal tumor of the cervix uteri is a rare cancer of cervix uteri derived from neural crest cells histologically composed of small round neoplatic cells with variable degree of neural glial and ependymal differentiation. Macroscopically the tumor is often a large soft poorly circumscribed mass with infiltrative borders and necrotic areas. It presents with dysfuntional vaginal bleeding or discharge lower abdominal pain and uterine enlargement.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version March 2024
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Primitive neuroectodermal tumor of the cervix uteri?
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