Bullous pyoderma gangrenosum
Synonyms: Phemphigoid pyoderma gangrenosum
A rare subtype of pyoderma gangrenosum disease characterized by grouped vesicles that rapidly spread and coalesce to form large bullae which evolve into ulcerations that have an erythematous peripheral halo and central necrosis mainly affecting the upper limbs and face. Lymphoproliferative diseases are frequently associated thus prognosis is often compromised.
Data from Orphanet are used to provide information on a disease's name, synonym(s), and overview.
Reference: Access aggregated data from Orphanet at Orphadata.
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on http://www.orphadata.org. Data version April 2024
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Bullous pyoderma gangrenosum?
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Advocacy Organizations
Autoinflammatory Alliance
https://autoinflammatory.org
Clinical Trials
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